Wild‐type (A, D, and G), F508del (B, E, and H), and G542X (C, F, and I ...
(A–I) Wild-type (A, D, G), Sema6B−/− (B, E, H), and Sema6C−/− ...
Wild-type (A, D, G, J), Sema6B−/− (B, E, H, K), and Sema6C−/− ...
(A) Wild type (a, c, e, g, i, k) and ddlc1ins1(b, d, f, h, j, l ...
Effects of TGF-β1 treatment on cultured wild-type (A, B, E, F, I, and ...
Characterization of two rat models of cystic fibrosis—KO and F508del ...
Decreased survival and growth rates of F508del and cystic fibrosis ...
Effect of TMA treatment on F508del CFTR transcription, expression, and ...
| Functional and biochemical defects in the lung of G542X CFTR rats ...
Nasal potential difference measurements in wild‐type (WT), F508del, and ...
| Effect of HIT1 on F508del CFTR trafficking and function. (A) Dose ...
Protein level of CFTR and CK2 in different wild-type (wt) and F508del ...
Wild type (WT, open symbols, N = 9) and heterozygous F508del (closed ...
Histochemical and immunocytochemical analysis of wild-type ( a, d, g ...
Representative traces of short‐circuit current in CFTR F508del and ...
Pieces of normal and F508del mutant murine ileal mucosa were incubated ...
The F508del mice were divided into four groups and received either ...
Histologic sections of adult (9-week-old) wild-type (a, d) and Foxe3 ...
Functional linkage between the Hsp27 and SUMO pathways. (A) F508del ...
Lung histological sections of wild-type (a,b,e,f,i,j) and CF mice ...
CFTR Localization in Native Airway Cells and Cell Lines Expressing Wild ...
Protein trafficking and electrophysiological assays revealed correction ...
Morphology of wild-type (A,D), gram (B,E), sty (C,F) and sty gram (G-I ...
| Airway hyperplasia and cellular infiltration in the lungs of ...
| Mice weights prior to (Day 0) and following 14-day treatment (Day 15 ...
Assessment of MCG1516A effects on processing and PM expression of ...
Activation of wild-type and F508del-CFTR chloride channel activity in ...
PMCA and SERCA2b interaction with wild-type or F508del-CFTR in human ...
Electron micrographs of brain capillaries in wild-type (a and c) and ...
| Rescue of functional F508del-CFTR Cl − currents in LUM/IVA and ...
Immunofluorescence staining of GBM of wild-type (A-D) and FcR-deficient ...
Generation of CFTRF508del/F508del and CFTRG542X/G542X sheep fetal ...
Frontiers | Stimulation of Wild-Type, F508del- and G551D-CFTR Chloride ...
Dose-response curves of wild-type (WT) and F508del-CFTR chloride ...
Figure S10. Comparison of the F508del/R1070F and F508del/R1070W cluster ...
Seedling phenotypes and developmental profile of fdl1-1 .... | Download ...
Ultrastructure of wild-type (a-d) and ΔHik34 mutant (e-h) cells grown ...
Table 1 from CFTR Localization in Native Airway Cells and Cell Lines ...
Immunoblot analysis of F508del-CFTR and WT-CFTR expression in HeLa ...
ROS and inflammatory cytokines control F508del-CFTR proteostasis via ...
Cell-based and electrophysiological assays demonstrate the ability of ...
(PDF) CFTR Localization in Native Airway Cells and Cell Lines ...
Transverse sections of anther locules from the wild-type (A-D) and the ...
Cell proliferation and myofibroblast differentiation in cultured lung ...
Immunolocalization of CFTR in parental, wt-CFTR and F508del-CFTR MDCK ...
The combined effect of VRT-325 and mutation on F508del- CFTR fails to ...
AFM images of fixed R. leguminosarum wild-type (a–d) and ctpA mutant ...
Aggregation of (a) the wild type, (b) R5G, and (c) R5E of Aβ42s ...
Wild-type (A-D,I,J,L,Q-T) and atk1-1 (E-H,K,M-P,U-X) male meiosis from ...
(PDF) Stimulation of Wild-Type, F508del- and G551D-CFTR Chloride ...
UV-VIS spectrograms of pigments from wild-type (a–d) and fusant F2-19 ...
Immunostaining for renin (brown) in wild type (A-D) and angiotensinogen ...
Immunofluorescence of cultured fibroblasts from wild-type (a and b ...
Expression of Noggin and Gremlin1 and its implications in fine-tuning ...
Schematic diagram depicting the phenotypes of Wild Type (A) and S-layer ...
Vascular pattern development in the first leaf of wild type (A-D) and ...
Double staining of Dm'h expression (in green) and BN3.1 (blue and red ...
| Generation of CF G542X rats. (A) A Cas9 sgRNA was designed to target ...
Calumenin or CFTR (green) in CFBE41o- wild-type or F508del cells were ...
F508del CFTR is detectable by immunostaining after low temperature ...
Expression of F508del induces chronic proteotoxic stress that affects ...
A SUMO-targeted ubiquitin ligase links F508del to the proteasome. (A ...
CRISPR strategy. A, For F508del rats, single‐guide RNA (sgRNA) was ...
F508del CFTR protein expression is increased in USG media, with similar ...
ELX-02 increases CFTR-dependent swelling in PDOs bearing a G542X ...
Targeting G542X CFTR nonsense alleles with ELX-02 restores CFTR ...
Mitochondrial membrane potential: hepatocytes from wild-type (A, D ...
A G542X cystic fibrosis mouse model for examining nonsense mutation ...
Primary F508del (CF) murine macrophages exhibit weak autophagic flux ...
Rescue of F508del short-circuit currents (Isc) in human airway ...
Maturation of F508del protein at low temperature. Pieces of ileal ...
F508del bone marrow-derived cells, specifically neutrophils, play an ...
CFTR response to calcium. (A–D) Representative traces of wild-type (A ...
Effect of triazole compounds in the F508del-CFTR genetic revertant 4RK ...
Confocal images of embryos of the wild-type (A–D),... | Download ...
F508del-CFTR trafficking correctors have mixed effects on the ...
Multi-omic comparisons between CFBE41o- cells stably expressing wild ...
Body weight (g, mean±s.e.m.) of wild-type, F508del-CFTR homozygous (CF ...
Rescue to the cell surface of a mature endogenous F508del-CFTR protein ...
Transverse sections of quiescent gastrocnemius muscle of wild-type ...
Unravelling the Regions of Mutant F508del-CFTR More Susceptible to the ...
VX-770 potentiated F508S-and F508C-CFTR similarly to F508del-CFTR ...
| Electrophysiological evaluation of F508del-CFTR inhibition by ...
Decoding F508del Misfolding in Cystic Fibrosis
Effect of peptides on F508del-CFTR activity in primary airway ...
Time-dependent flash-induced fluorescence yield of the wild-type (A ...
Sciatic nerve ligation experiment. Sciatic nerves of wild-type (a-d ...
Some F508del-CFTR correctors correct the trafficking of hERG G601S ...
(PDF) Correcting the F508del-CFTR variant by modulating eukaryotic ...
Increased microtubule acetylation in CF/HDA mice. Nasal epithelium from ...
Phenotypes of clv3-2 phb phv cna plants. Shown are wild-type (A,D ...
Role of CFTR expressed by neutrophils in modulating acute lung ...
Floral organ phenotypes in wild-type (A,E,I,J), w6 (B,F,K), w3 ...
Endogenous myoJ is concentrated on contractile vacuole membranes. Shown ...
(PDF) Identification of a novel water-soluble activator of wild-type ...
srp embryos partially differentiate Malpighian tubules. Wild-type (A-D ...
Elexacaftor/tezacaftor/ivacaftor efficacy in intestinal organoids with ...
Discovery of Pyrrolo[2,3-b]pyrazines Derivatives as Submicromolar ...
Targeting F508del-CFTR to develop rational new therapies for cystic ...
Brassinosteroid coordinates cell layer interactions in plants via cell ...
RNA polymerase II transcription initiation in holo-TFIID-depleted mouse ...
Adenine base editing with engineered virus-like particles rescues the ...
The L467F-F508del Complex Allele Hampers Pharmacological Rescue of ...
Normal GC morphogenesis in CDKA function mutants. Corresponding ...
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Regulated tissue fluidity steers zebrafish body elongation - PMC
Gene Expression Image Detail
